Skip to main content

Table 1 Systemic scoring system for SJIA patients.

From: Correlation analyses of clinical and molecular findings identify candidate biological pathways in systemic juvenile idiopathic arthritis

Score

Severity level

Systemic symptoms

0

None

No active disease

1

Mild

Having any one of the following: rash, fevers < 10 days in the past month, ESR 40 to 90, platelets > 450,000

2

Moderate

Having at least three of the following: rash, fever > 10 days in the past month, WBC > 20,000, ESR > 90, platelets > 550,000, d-dimers 250 to 500, elevated fibrinogen

3

Severe

Having any one of the following symptoms: pneumonitis, percarditis, pleural effusion, Macrophage Activation Syndrome (MAS)