Variable | All CTD | Stratified Group 1 | Stratified Group 2 | Stratified Group 3 |
---|---|---|---|---|
Units are percentage unless stated | (n = 203 unless stated) | (n = 15 unless stated) | (n = 138 unless stated) | (n = 50 unless stated) |
Median age, years | 58 | 58 | 59 | 53 |
Male/female | 63/140 | 2/13 | 47/91 | 14/36 |
Survival (alive/dead) | 131/72 | 14/1 | 95/43 | 22/28 |
Never/ex-smokers | 122/76 | 9/6 | 83/52 | 30/18 |
Follow-up time, months | 45.9 ± 24.0 | 57.8 ± 15.3 | 47.4 ± 22.2 | 38.1 ± 28.5 |
FEV1 % predicted | 68.7 ± 18.4 (184) | 79.5 ± 14.7 (14) | 71.4 ± 18.3 (122) | 58.7 ± 15.4 (48) |
FVC % predicted | 70.8 ± 20.9 (184) | 88.3 ± 15.6 (14) | 74.4 ± 20.7 (122) | 56.7 ± 13.9 (48) |
DLco % predicted | 39.3 ± 14.2 (189) | 54.5 ± 14.4 (14) | 41.6 ± 13.0 (129) | 28.4 ± 9.8 (46) |
Kco % predicted | 66.1 ± 17.6 (189) | 72.2 ± 17.4 (14) | 68.0 ± 16.8 (129) | 58.9 ± 18.0 (46) |
TLC % predicted | 70.9 ± 16.7 (175) | 89.6 ± 13.6 (13) | 72.7 ± 16.0 (121) | 59.4 ± 11.2 (41) |
CPI | 51.2 ± 13.7 (180) | 35.8 ± 11.9 (14) | 48.6 ± 12.6 (120) | 62.7 ± 8.0 (46) |
CALIPER ILD extent | 20.2 ± 18.3 | 2.4 ± 2.1 | 12.7 ± 8.7 | 46.2 ± 15.0 |
CALIPER Fibrosis extent | 5.5 ± 5.2 | 0.7 ± 0.5 | 4.0 ± 3.4 | 11.0 ± 5.9 |
CALIPER GGO | 14.7 ± 15.7 | 1.7 ± 1.9 | 8.7 ± 7.8 | 35.2 ± 16.3 |
CALIPER Reticular pattern | 4.9 ± 4.6 | 0.6 ± 0.4 | 3.7 ± 3.0 | 9.8 ± 5.3 |
CALIPER Honeycombing | 0.6 ± 1.5 | 0.1 ± 0.1 | 0.4 ± 0.7 | 1.2 ± 2.8 |
CALIPER Emphysema | 0.6 ± 2.8 | 0.1 ± 0.1 | 0.9 ± 3.3 | 0.2 ± 0.7 |
CALIPER PVV | 4.2 ± 1.7 | 2.5 ± 0.5 | 3.6 ± 1.1 | 6.5 ± 1.3 |
CALIPER Normal lung | 74.9 ± 19.5 | 95.1 ± 2.3 | 82.8 ± 9.5 | 47.1 ± 15.2 |
Visual ILD extent | 53.5 ± 24.8 | 43.1 ± 28.4 | 47.4 ± 23.0 | 73.5 ± 17.0 |
Visual fibrosis extent | 31.7 ± 19.9 | 7.2 ± 6.9 | 27.6 ± 16.4 | 50.6 ± 16.7 |
Visual GGO | 20.7 ± 20.0 | 34.1 ± 28.8 | 18.9 ± 19.1 | 21.7 ± 17.9 |
Visual reticular pattern | 27.6 ± 17.9 | 7.2 ± 6.9 | 24.9 ± 15.4 | 41.1 ± 17.7 |
Visual honeycombing | 4.1 ± 9.3 | 0.0 ± 0.0 | 2.7 ± 6.6 | 9.4 ± 14.1 |
Visual consolidation | 0.6 ± 2.3 | 1.8 ± 4.9 | 0.6 ± 2.2 | 0.4 ± 1.0 |
Visual emphysema | 4.1 ± 10.7 | 5.0 ± 16.9 | 3.8 ± 9.8 | 4.8 ± 10.9 |
Visual mosaicism | 1.7 ± 4.9 | 3.9 ± 8.1 | 1.4 ± 4.9 | 1.9 ± 3.6 |
Visual TxBx (max score 18) | 5.5 ± 3.7 | 1.0 ± 1.2 | 5.1 ± 3.4 | 7.9 ± 3.6 |
Main PA diameter, mm | 31.0 ± 4.8 | 28.7 ± 4.0 | 30.4 ± 4.3 | 33.3 ± 5.6 |
AAo diameter, mm | 32.0 ± 4.0 | 31.9 ± 3.3 | 31.8 ± 4.0 | 32.7 ± 4.0 |
RVSP, mmHg | 39.2 ± 16.1 (100) | 28.9 ± 3.8 (7) | 37.0 ± 14.7 (62) | 45.8 ± 18.1 (31) |